X-Linked Lymphoproliferative Disease Presenting as Pancytopenia in a 10-Month-Old Boy
نویسندگان
چکیده
X-linked lymphoproliferative disease, also known as Duncan's syndrome, is a rare genetic disorder that causes exaggerated immune responses to Epstein-Barr virus (EBV) infection and often leads to death. Patient presentation varies but can include signs and symptoms typical of EBV, pancytopenia, and fulminant hepatitis.
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عنوان ژورنال:
دوره 2010 شماره
صفحات -
تاریخ انتشار 2010